Keratoderma blennorrhagicumlike rash masquerading as contact dermatitis. Kertatoderma can be inherited, acquired, and rarely, paraneoplastic ie secondary to an internal malignancy. If you have problems viewing pdf files, download the latest version of adobe reader. The relationship of the cutaneous manifestations to the syndrome following some cases of gonorrhea was first described by vidal 1 in 1893. Palmoplantar keratoderma primary care dermatology society uk. Pdf on jan 1, 2008, dimitar gospodinov and others published keratoderma blenorrhagicum in a. Acquired palmoplantar keratoderma is more likely to present in adulthood. The presence of keratoderma blennorrhagica is diagnostic of reactive arthritis in the. She reported morning stiffness exceeding 1 hour that decreased with physical activity, worsened with rest, but improved with administration of nonsteroidal antiinflammatory drugs nsaids. For language access assistance, contact the ncats public information officer. Keratoderma blennorrhagicum pictures, symptoms, treatment. Disease bioinformatics research of keratoderma blenorrhagica has been linked to arthritis, reactive, keratosis, reiter syndrome, arthritis, psoriasis. Keratoderma blennorrhagicum definition of keratoderma.
In recent years, speculation has arisen that a molecular genetic classification system will replace the traditional, clinically based, descriptive systems. Keratoderma blennorrhagica also known as keratosis blennorrhagica, it is a type of skin disease where scaly rashes are found on palms and soles. Keratoderma blennorrhagicum an overview sciencedirect. Manual of rheumatology and outpatient orthopedic disorders. Pronunciation of keratoderma blennorrhagica with 3 audio pronunciations, 2 synonyms, 2 translations and more for. She reported morning stiffness exceeding 1 hour that decreased with physical activity, worsened with rest, but improved with administration of nonsteroidal antiinflammatory drugs. This page will undergo revision to reflect the name change. Keratosis blennorrhagica medical definition merriam. Keratoderma blennorrhagicumlike rash this article has no abstract. Jun 28, 2017 punctate palmoplantar keratoderma type i is a rare condition that affects the skin. The relationship of the cutaneous manifestations to the syndrome following some cases of gonorrhea was first described by vidal1 in 1893. Thefollowing, acaseofkeratodermablennorrhagicum, seems to present some special points.
Palmoplantar keratoderma is also sometimes known as keratosis palmaris et plantaris. Keratoderma blennorrhagica is a painless desquamative psoriaticlike papulosquamous eruption and is sometimes referred to as pustulosis palmoplantaris and occurs on the palms and soles of the feet. Pronunciation of keratoderma blennorrhagica with 3 audio pronunciations, 2 synonyms, 2 translations and more for keratoderma blennorrhagica. Notable labs included positive hiv assay with an absolute cd4 count of 6 and a viral load over 750,000 copies and a negative rpr. Idiopathic acquired palmoplantar keratoderma in a patient with no. The exact cause that leads to the appearance of the reiter syndrome has yet to be identified but it seems there is a genetic predisposition. It can be caused by genetic abnormalities which are passed down through families in an autosomal dominant or autosomal recessive pattern. Keratoderma blennorrhagica an overview sciencedirect. Palmoplantar keratoderma ppk constitutes a heterogeneous group of disorders characterized by thickening of the palms and the soles of individuals who are affected. Keratoderma definition of keratoderma by the free dictionary. The appearance is usually of a vesicopustular waxy lesion with a yellow brown colour. Keratoderma blennorrhagicum describes the appearance of skin lesions resembling psoriasis that appear first on the palms of the hands and soles of the feet but may eventually spread to the scalp, torso, and genitals.
Please tell us where you read or heard it including the quote, if possible. Keratoderma blennorrhagicum medical condition youtube. Punctate palmoplantar keratoderma type i genetic and. Recently pleuropneumonialike organisms have been suspected of being causative agents. What is reiter syndrome reiter syndrome has been reclassified as reactive arthritis and is a type of spondyloarthropathy. Pdf reiters syndrome is a systemic disorder, originally occurs as a triad of arthritis, urethritis and conjunctivitis.
Syndroma reiter, keratoderma blenorrhagicum introduction reiter syndrome, also known as reactive arthritis, is a disease in which a nonsuppurative polyarthritis lasting more then one month follows closely a lower urogenital or enteric infection. Palmoplantar keratoderma as a presenting sign of primary biliary cirrhosis. Palmoplantar refers to the skin on the soles of the feet and palms of the hands. Apr 30, 2020 keratoderma is an inherited genetic disorder. The foremost finding was genital ulceration in rea which can be included among disorders causing genital ulceration and must be kept in the differential diagnosis of genital ulceration. Clinically there is a bilateral yellow thickening of the skin. Seronegative spondyloarthropathies and sapho syndrome. Palmoplantar keratoderma and spastic paraplegia also known as charcotmarietooth disease with palmoplantar keratoderma and nail dystrophy is an autosomal dominant or xlinked dominant condition that begins in early childhood with thick focal keratoderma.
Ppk can be either acquired during the lifetime more commonly or inherited. Palmoplantar keratodermas ppks are a diverse entity of disorders that are characterized by abnormal thickening of the skin on the palms and soles. Keratoderma climactericum definition of keratoderma. Given the sexual history and rapidity of the symptoms, an hiv and syphilis test w ere performed. Later lesions of keratoderma blennorrhagicum usually do not contain spongiform pustules but reveal the nonspecific findings of acanthosis, hyperkeratosis, and parakeratosis. Apr 27, 2015 keratoderma blennorrhagicum are skin lesions commonly found on the palms and soles but which may spread to the scrotum, scalp and trunk this video contains general medical information if in doubt.
The problems posed by the etiology and treatment of keratosis blennorrhagica are well known. Keratoderma definition of keratoderma by medical dictionary. Ppk can also be a feature of various underlying syndromes. It is characterized by an aseptic rheumatoid factornegative asymmetric polyarthritis that may be accompanied by conjunctivitis, a rash of the extremities keratoderma blennorrhagica, andor painless oral ulcers. Mar 20, 2018 the prognosis of acquired keratoderma depends upon the severity of the symptoms, the response to treatment, and most importantly upon the severity of the underlying condition who gets acquired keratoderma. Keratoderma blennorrhagica as first presenting symptom of. Keratoderma blennorrhagicum is a rare skin disease. Punctate palmoplantar keratoderma type i genetic and rare. Keratoderma blennorrhagica as a result of reactive. Keratoderma is a term that means marked thickening of the skin. Interesting clinical features of rea are keratoderma blennorrhagicum, pustulosis. A 26yearold woman, previously healthy, that a month ago started complaining of pain in the soles of both feet, which followed, additionally, to the right knee, the left knee, left elbow and right shoulder. A close but indeterminate relation to gonorrhea exists in many, but not all, cases. Acquired keratoderma is a palmoplantar keratoderma that is not inherited as a primary genetic condition.
This chapter provides a practical overview of keratoderma, and is set out as below. In rare forms of ppk, organs other than the skin may also be affected. Age and sex distribution acquired keratoderma may be observed in a wider age range of individuals. Oct 14, 2016 early lesions of keratoderma blennorrhagicum feature a spongiform pustule in the upper dermis.
Keratoderma climactericum refers to the form that occurs during the menopausal period. Pdf on feb 1, 1994, f g inglis and others published reiters disease, keratoderma blennorrhagica and rapidly progressive crescentic iga glomerulonephritis find, read and cite all the research. Media in category keratoderma blennorrhagicum the following 3 files are in this category, out of 3 total. This condition is a symptom of reactive arthritis joint pain due to an infection, which is itself a component of a systemic disease known as reiters syndrome. Request pdf treatment of keratoderma blennorrhagicum with tazarotene gel 0. Classically it includes the triad arthritis, urethritis, and conjunctivitis. A 55yearold bisexual man presented with a few weeks history of lethargy followed by the onset of a widespread nonpruritic rash that covered much of his body, including the palms panel a. Keratoderma blennorrhagica keratoderma blennorrhagica. Sep 27, 2016 keratoderma climactericum is a type of acquired palmoplantar keratoderma. Palmoplantar keratoderma ppk is a group of skin conditions characterized by thickening of the skin on the palms of the hands and soles of the feet. Palmoplantar keratoderma is a term used to define a marked thickening of the skin on the palms and soles, either as a focal entity, or diffuse. Tonna and laing may 15 issue 1 describe a patient with secondary syphilis. These lesions may spread to the scrotum, scalp and trunk.
There are many forms of keratoderma which is the term given to the development of harmless skin thickening on the soles, particularly the heels. Keratoderma climactericum is a type of acquired palmoplantar keratoderma. Keratoderma blennorrhagicum appears, as it was already mentioned, in the genitourinary variant of the reiter syndrome or reactive arthritis. Keratinization disorder which presents at birth with generalized erythema, widespread bullae and desquamation resulting in denuded skin form of ichthyosis, an abnormality of epidermal maturation resulting in skin fragility epidermolytic hyperkeratosis is a descriptive term which refers to specific microscopic features i. Keratoderma blennorrhagicum, british journal of dermatology. Mar 06, 2018 keratoderma blennorrhagicum is a skin condition associated with reactive arthritis formerly known as reiter syndrome, according to mddk. Keratoderma medical definition merriamwebster medical. We report the case of a 34yearold man who presented with a twomonth history of painful keratotic plaques that involved the skin surrounding. Keratoderma blenorrhagicum skin lesions a week after their appearance.
Current concepts in diagnosing and treating keratoderma. The study of keratoderma blenorrhagica has been mentioned in research publications which can be found using our bioinformatics tool below. Reactive arthritis, formerly known as reiters syndrome, is a form of inflammatory arthritis that. Treatment of keratoderma blennorrhagicum with tazarotene. Read keratoderma blennorrhagicum, british journal of dermatology on deepdyve, the largest online rental service for scholarly research with thousands of academic publications available at your fingertips. Keratoderma blennorrhagicum is a skin condition associated with reactive arthritis formerly known as reiter syndrome, according to mddk. The rash was diagnosed as keratoderma blennorrhagica and the patient was diagnosed with aids. Reiter syndrome is a collection of symptoms but generally has three main features. Keratoderma blennorrhagicum is an interesting dermatosis associated with gonorrheal arthritis and occurs almost exclusively in the male sex, although three cases have been reported in females by lees, 1 issac 2 and robert.
Keratoderma blennorrhagicum is commonly seen as an additional feature of reactive arthritis in almost 15% of male patients. It can occur in the first few months of life and almost always presents by age 3. His rheumatologic evaluation confirmed decreased range of motion at the spine with an abnormal occiput to wall test of 8 cm, abnormal schobers test 1012 cm increase with flexion and no reversal of lumbar lordosis, and decreased excursion in lateral bending. For claims with a date of service on or after october 1, 2015, use an equivalent icd10cm code or codes. Learn vocabulary, terms, and more with flashcards, games, and other study tools. What are the causes of punctatetype palmoplantar keratoderma. Palmoplantar keratoderma as a presenting sign of primary. Dec 29, 2016 palmoplantar keratoderma ppk is a group of skin conditions characterized by thickening of the skin on the palms of the hands and soles of the feet. It is a subtype of punctate palmoplantar keratoderma. Keratoderma blennorrhagica an overview sciencedirect topics. Keratoderma blennorrhagicum etymologically meaning keratinized kerato skin derma. This health issue is characterized by the presentation of a rash that begins at the extremities and spreads inward slowly and steadily.
Punctate palmoplantar keratoderma type i is a rare condition that affects the skin. Palmoplantar keratoderma is the name given to a group of conditions where there is abnormal thickening of the skin on the palms of the hands and soles of the feet. Punctate keratoderma this ladys daughter had exactly the same lesions. Keratoderma blennorrhagica is a painless desquamative psoriaticlike papulosquamous eruption. Keratoderma blennorrhagicum are skin lesions commonly found on the palms and soles but which may spread to the scrotum, scalp and trunk this video contains general medical information if in doubt. Geisler, in infectious diseases fourth edition, 2017. Only seventy cases are on record, of which eleven have been described in the american literature. This keratosis of the palms and soles appears late in women of menopausal age. The most common skin findings are palmoplantar keratoderma, circinate balanitis or vulvitis, psoriasislike skin lesions, and buccal ulcerations1,2. Keratoderma blennorrhagicum an overview sciencedirect topics. A read is counted each time someone views a publication summary such as the title, abstract, and list of authors, clicks on a figure, or views or downloads the fulltext. Ppk can be either acquired during the lifetime more commonly. It may occur as part of a generalised skin condition some of which may be inherited or as a result of another illness. These lesions may join together to form larger crusty plaques with desquamating edges.
Rubenstein md, frcpc, in imaging of arthritis and metabolic bone disease, 2009. Keratoderma blennorrhagicum everything you need to know. Keratoderma blennorrhagica definition of keratoderma. Etiology punctatetype palmoplantar keratoderma is a genetic disorder. Treatment of keratoderma blennorrhagicum with tazarotene gel. Palmoplantar keratoderma genetic and rare diseases. Reactive arthritis is a rare complication of genital chlamydia.
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